{"id":6419,"date":"2020-07-06T17:25:54","date_gmt":"2020-07-06T17:25:54","guid":{"rendered":"http:\/\/www.vorsteh.is\/?page_id=6419"},"modified":"2020-07-06T17:40:35","modified_gmt":"2020-07-06T17:40:35","slug":"von-willebrand-sjukdomur","status":"publish","type":"page","link":"https:\/\/www.vorsteh.is\/?page_id=6419","title":{"rendered":"von Willebrand sj\u00fakd\u00f3mur"},"content":{"rendered":"\n<p><strong>Hva\u00f0 er von Willebrand (vWD)?<\/strong><\/p>\n\n\n\n<p>Von Willebrand sj\u00fakd\u00f3mur (skammstafa\u00f0 vWD) er\nalgengastur allra bl\u00e6\u00f0ingasj\u00fakd\u00f3ma. <\/p>\n\n\n\n<p>Vandam\u00e1li\u00f0 tengist pr\u00f3teini \u00ed bl\u00f3\u00f0i sem kallast von Willebrand\nfaktor, skammstafa\u00f0 vWF. Von Willebrand faktor er nau\u00f0synlegur til \u00feess a\u00f0 bl\u00f3\u00f0storknun\ns\u00e9 e\u00f0lileg.<\/p>\n\n\n\n<p>Hundur me\u00f0 von Willebrand sj\u00fakd\u00f3m hefur anna\u00f0 hvort ekki n\u00f3g af\n\u00feessum storku\u00fe\u00e6tti e\u00f0a hann virkar ekki sem skyldi.<\/p>\n\n\n\n<p><strong>\u00derj\u00e1r\na\u00f0alger\u00f0ir von Willebrand sj\u00fakd\u00f3ms:<\/strong><\/p>\n\n\n\n<ul class=\"wp-block-list\"><li>Type 1:\nAlgengasta form sj\u00fakd\u00f3msins; magn vWF er l\u00e1gt en bygging faktorsins e\u00f0lileg<\/li><li><strong>Type 2: Bygging faktorsins er \u00f3e\u00f0lileg. Pr\u00f3teini\u00f0\ner of stutt og l\u00edtur \u00f6\u00f0ruv\u00edsi \u00fat en e\u00f0lilegt pr\u00f3tein <\/strong><\/li><li>Type 3:\nAlvarlegasta ger\u00f0 vWD; vWF skortir alveg. \u00dea\u00f0 veldur einnig \u00fev\u00ed a\u00f0 faktor VIII\ner \u00ed mj\u00f6g litlum m\u00e6li \u00ed bl\u00f3\u00f0i. \u00deessi ger\u00f0 er sjaldg\u00e6fust.<\/li><\/ul>\n\n\n\n<p><strong>Einkenni:<\/strong><\/p>\n\n\n\n<p>Einkenni vWD geta veri\u00f0 v\u00e6g\nog alveg upp \u00ed alvarlega tilhneigingu \u00e1 bl\u00e6\u00f0ingum. Hundar geta ,,bori\u00f0\u201d eiginleika\nvWD \u00e1n \u00feess a\u00f0 tj\u00e1 bl\u00e6\u00f0ingartilhneigingu. Alvarlegt vWD getur valdi\u00f0 skyndilegri\nog sj\u00e1lfsprottinni bl\u00e6\u00f0ingu \u00far nefi, munni, \u00fevag-, \u00e6xlunar- og meltingarf\u00e6rum.\n\u00d3st\u00f6\u00f0vandi e\u00f0a \u00f3h\u00f3fleg bl\u00e6\u00f0ing eftir a\u00f0ger\u00f0ir. Eins getur or\u00f0i\u00f0 \u00f3h\u00f3fleg bl\u00e6\u00f0ing\nvi\u00f0 klippingu kl\u00f3a og \u00ed tannskiptum hj\u00e1 hvolpum sem eru me\u00f0 vWD, \u00e1samt\nalvarlegum bl\u00e6\u00f0ingum hj\u00e1 t\u00edkum \u00ed og eftir got. S\u00fdkingar, innkirtlasj\u00fakd\u00f3mar og\n\u00e1kve\u00f0in lyf geta auki\u00f0 tilhneigingu \u00e1 bl\u00e6\u00f0ingum hj\u00e1 hundum me\u00f0 vWD.<\/p>\n\n\n\n<p><strong>Greining:<\/strong><\/p>\n\n\n\n<p>Von Willebrand er greint\nme\u00f0 DNA pr\u00f3fi. <\/p>\n\n\n\n<p><strong>Hvernig erfist von\nWillebrand?<\/strong><\/p>\n\n\n\n<p>DNA pr\u00f3f gefur \u00ferj\u00e1r\nm\u00f6gulegar ni\u00f0urst\u00f6\u00f0ur um a\u00f0 hundur s\u00e9:<\/p>\n\n\n\n<ol class=\"wp-block-list\"><li>S\u00fdktur (affected) <\/li><li>Beri (Carrier)<\/li><li>Hreinn (Clear) N\/C<\/li><\/ol>\n\n\n\n<p>H\u00e9r m\u00e1 sj\u00e1 t\u00f6flu um hvernig vWD erfist:<\/p>\n\n\n\n<figure class=\"wp-block-image is-resized\"><img loading=\"lazy\" decoding=\"async\" src=\"http:\/\/www.vorsteh.is\/wp-content\/uploads\/2020\/07\/sk\u00fdringamynd-vWD-1024x596.jpg\" alt=\"\" class=\"wp-image-6420\" width=\"797\" height=\"463\" srcset=\"https:\/\/www.vorsteh.is\/wp-content\/uploads\/2020\/07\/sk\u00fdringamynd-vWD-1024x596.jpg 1024w, https:\/\/www.vorsteh.is\/wp-content\/uploads\/2020\/07\/sk\u00fdringamynd-vWD-300x175.jpg 300w, https:\/\/www.vorsteh.is\/wp-content\/uploads\/2020\/07\/sk\u00fdringamynd-vWD-768x447.jpg 768w, https:\/\/www.vorsteh.is\/wp-content\/uploads\/2020\/07\/sk\u00fdringamynd-vWD.jpg 1199w\" sizes=\"auto, (max-width: 797px) 100vw, 797px\" \/><figcaption><br> <br><\/figcaption><\/figure>\n\n\n\n<p>Eftirfarandi er \u00far Reglum um skr\u00e1ningu \u00ed \u00e6ttb\u00f3k hj\u00e1 HRF\u00cd var\u00f0andi afkv\u00e6mi sem teljast arfhrin (N\/C\/P) og tekur gildi 1.jan\u00faar 2021<\/p>\n\n\n\n<p><em>Eftirfarandi gildir um undaneldisd\u00fdr og ni\u00f0urst\u00f6\u00f0ur DNA pr\u00f3fa vegna sj\u00fakd\u00f3ma nema anna\u00f0 s\u00e9 teki\u00f0 fram um einst\u00f6k hundakyn: Bera m\u00e1 einungis nota \u00ed r\u00e6ktun \u00e1 m\u00f3ti arfhreinum hundum. S\u00fdktir hundar eru settir \u00ed r\u00e6ktunarbann. \u00cd \u00feeim tilvikum \u00fear sem b\u00e1\u00f0ir foreldrar eru me\u00f0 DNA ni\u00f0urst\u00f6\u00f0 fr\u00edir 2 (Normal\/Clear; N\/C), telst afkv\u00e6mi arfhreint fyrir \u00feeirri ger\u00f0 (Normal\/Clear by Parentage; N\/C\/P). DNA pr\u00f3fa \u00fearf n\u00e6stu kynsl\u00f3\u00f0 \u00e1 eftir.<\/em><\/p>\n\n\n\n<p>Heimildir af s\u00ed\u00f0u:<\/p>\n\n\n\n<p>Bl\u00e6\u00f0arami\u00f0st\u00f6\u00f0 LSH<\/p>\n\n\n\n<p>Cornell University College of\nVeterinary Medicine<\/p>\n\n\n\n<p>AnimaLabs<\/p>\n\n\n\n<p>Hundar\u00e6ktarf\u00e9lags \u00cdslands<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Hva\u00f0 er von Willebrand (vWD)? Von Willebrand sj\u00fakd\u00f3mur (skammstafa\u00f0 vWD) er algengastur allra bl\u00e6\u00f0ingasj\u00fakd\u00f3ma. Vandam\u00e1li\u00f0 tengist pr\u00f3teini \u00ed bl\u00f3\u00f0i sem kallast von Willebrand faktor, skammstafa\u00f0 vWF. Von Willebrand faktor er nau\u00f0synlegur til \u00feess a\u00f0 bl\u00f3\u00f0storknun s\u00e9 e\u00f0lileg. Hundur me\u00f0 von &hellip; <a href=\"https:\/\/www.vorsteh.is\/?page_id=6419\">Halda \u00e1fram a\u00f0 lesa <span class=\"meta-nav\">&rarr;<\/span><\/a><\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"ngg_post_thumbnail":0,"_mc_calendar":[],"footnotes":""},"class_list":["post-6419","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=\/wp\/v2\/pages\/6419","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=6419"}],"version-history":[{"count":4,"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=\/wp\/v2\/pages\/6419\/revisions"}],"predecessor-version":[{"id":6425,"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=\/wp\/v2\/pages\/6419\/revisions\/6425"}],"wp:attachment":[{"href":"https:\/\/www.vorsteh.is\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=6419"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}